Kata Kunci

Abstrak

Biliary atresia (BA) is a condition of biliary obstruction. Kasai portoenterostomy (KPE) is a treatment option. The aim is to determine the success rate of the Kasai procedure and prognosis in BA patients with other underlying diseases. This is a descriptive case study research. We report a boy, 2 months and 11 days, with jaundice all over his body since one week old; putty stool, and dark urine. The child had an old man's face, icteric appearance, rib xylophone, subcostal retraction, rales, continuous heart murmur, and wasting. Total and direct bilirubin, SGOT, SGPT, and gamma GT levels were increased. A Kasai surgical procedure was carried out but did not significantly improve his condition because the operation was performed at the age of 4 months and 8 days, with liver cirrhosis, sepsis, pneumonia, and malnutrition. Cytomegalovirus (CMV) infection and acyanotic congenital heart disease also worsened his preoperative condition. Kasai portoenterostomy is a method of managing biliary atresia, but our patient was diagnosed with biliary atresia accompanied by CMV infection, congenital heart disease, and pneumonia. Therefore, the procedure was not sufficient for this condition, and the mortality rate is higher than in cases of biliary atresia alone. The age at the time of surgery also influences the prognosis.